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Budd-Chiari Syndrome

What is Budd-Chiari Syndrome?

Budd-Chiari syndrome is a rare disorder characterized by the blockage of the veins that transport the blood out from the liver. As a consequence, the blood flow is blocked and the blood accumulates in the liver causing an enlargement of the liver (hepatomegaly). The excess of fluid may leak into the abdominal cavity forming fluid accumulations that cause the abdomen to swell, a condition called ascites.

Symptoms of the syndrome include abdominal pain, jaundice (a yellow coloring of the skin and white part of the eyes) and high blood pressure of the main veins of the liver (portal hypertension).

If left untreated the condition might worsen to cause damage and scarrring (cirrhosis) of the liver and eventually cause life-threatening liver failure. The treatment will vary depending on what is the underlying cause of the vein obstruction. Sometimes an anticoagulant therapy is enough to prevent the formation of blood clots that block the blood flow. Some patients might require a surgical intervention. If cirrhosis has already occurred, a liver transplantation might be needed.

 

Budd-Chiari syndrome is a rare disorder characterized by the blockage of the veins that transport the blood out from the liver. As a consequence, the blood flow is blocked and the blood accumulates in the liver causing an enlargement of the liver (hepatomegaly). The excess of fluid may leak into the abdominal cavity forming fluid accumulations that cause the abdomen to swell, a condition called ascites.

Symptoms of the syndrome include abdominal pain, jaundice (a yellow coloring of the skin and white part of the eyes) and high blood pressure of the main veins of the liver (portal hypertension).

If left untreated the condition might worsen to cause damage and scarrring (cirrhosis) of the liver and eventually cause life-threatening liver failure. The treatment will vary depending on what is the underlying cause of the vein obstruction. Sometimes an anticoagulant therapy is enough to prevent the formation of blood clots that block the blood flow. Some patients might require a surgical intervention. If cirrhosis has already occurred, a liver transplantation might be needed.

Acknowledgement of Budd-Chiari Syndrome has not been added yet.

1.5http://www.orpha.net

Synonyms for Budd-Chiari Syndrome has not been added yet.
Cause of Budd-Chiari Syndrome has not been added yet.
Symptoms for Budd-Chiari Syndrome has not been added yet.
Diagnosis of Budd-Chiari Syndrome has not been added yet.
Diagnostic tests of Budd-Chiari Syndrome has not been added yet
Treatments of Budd-Chiari Syndrome has not been added yet.
Prognosis of Budd-Chiari Syndrome has not been added yet.
Tips or Suggestions of Budd-Chiari Syndrome has not been added yet.
References of Budd-Chiari Syndrome has not been added yet.
hi Created by kjsjd
Last updated 6 Jan 2012, 09:11 PM

Posted by kjsjd
6 Jan 2012, 09:11 PM

my son has just had acute buddchiari and been very unwell - no cause yet found, although he does also have renal disease as well - and underwent a successful tipps procedure for this. all ok at the moment although will be on warfarin lifelong i am told...

Budd chiari treatments Created by mstadendorff
Last updated 20 May 2009, 11:44 AM

Posted by mstadendorff
20 May 2009, 11:44 AM

Hi I just want to know if there is not maybe any new treatments out there for budd chiari, or any advice?

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hi

Created by kjsjd | Last updated 6 Jan 2012, 09:11 PM

Budd chiari treatments

Created by mstadendorff | Last updated 20 May 2009, 11:44 AM


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