My son was diagnosed with hearing loss associated with Type I WS shortly after birth. Now at 8 months of age it appears his hearing loss may be progressing, which is not typical. Anyone else have experience with this?

yes, I have progressive profound deafness. The doctors did biopsies of my intestines, He believes with the aganglionosis I have type IV.

Thanks for the response. After more evaluations, it appears we had one bad audiological evaluation. Switching audiologists made all the difference! For now, at least, the Type I diagnosis remains.